{
  "id": 19414,
  "label": "acquired angioedema",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0019624",
  "properties": {
    "xrefs": [
      "DOID:0080941",
      "GARD:0008605",
      "MEDGEN:419486",
      "MESH:C538173",
      "Orphanet:91385",
      "UMLS:C2931758",
      "icd11.foundation:1078767412"
    ],
    "synonyms": [
      "AAE",
      "acquired C1 inhibitor deficiency",
      "acquired angioedema",
      "acquired angioneurotic edema",
      "acquired angioneurotic oedema",
      "acquired bradykinine-induced angioedema",
      "acquired non histamine-induced angioedema",
      "angioedema, acquired"
    ],
    "categories": [
      {
        "ref": "MONDO:0002051",
        "name": "integumentary system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      }
    ],
    "definition": "Acquired angioedema (AAE) is characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain due to an acquired C1 inhibitor (C1-INH) deficiency."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 5,
  "parents": [
    {
      "id": 11639,
      "label": "angioedema",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        7148,
        19142
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "CSP:2716-7007",
          "DOID:1558",
          "EFO:0005532",
          "HP:0100665",
          "ICD9:995.1",
          "MEDGEN:1543",
          "MESH:D000799",
          "SCTID:400075008",
          "UMLS:C0002994"
        ],
        "synonyms": [
          "Edemas, angioneurotic",
          "Quincke edema",
          "Quincke oedema",
          "Quincke's edema",
          "Quincke's oedema",
          "Quinckes edema",
          "Quinckes oedema",
          "Urticarias, giant",
          "angioedemas",
          "angioneurotic Edemas",
          "edema, Quincke's",
          "edema, angioneurotic",
          "giant Urticarias",
          "giant urticaria",
          "urticaria, giant",
          "angioneurotic edema",
          "angioneurotic oedema"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Swelling involving the deep dermis, subcutaneous, or submucosal tissues, representing localized edema. Angioedema often occurs in the face, lips, tongue, and larynx."
      },
      "child_count": 6,
      "reference_id": "MONDO:0010481"
    }
  ],
  "children": [
    {
      "id": 16030,
      "label": "acquired angioedema type 2",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        19414
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0019747",
          "MEDGEN:1814461",
          "Orphanet:100055",
          "UMLS:C5680381"
        ],
        "synonyms": [
          "AAE 2",
          "AAE II",
          "acquired angioneurotic edema type 2",
          "acquired angioneurotic oedema type 2"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Acquired angioedema type 2 (AAE2) is a type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway."
      },
      "child_count": 0,
      "reference_id": "MONDO:0015055"
    },
    {
      "id": 16031,
      "label": "acquired angioedema type 1",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        19414
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0019748",
          "MEDGEN:1814460",
          "Orphanet:100056",
          "UMLS:C5680380"
        ],
        "synonyms": [
          "acquired angioneurotic edema type 1",
          "acquired angioneurotic oedema type 1"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Acquired angioedema type 1 (AAE 1) is a type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway."
      },
      "child_count": 0,
      "reference_id": "MONDO:0015056"
    },
    {
      "id": 16032,
      "label": "renin-angiotensin-aldosterone system-blocker-induced angioedema",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        19414
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0016936",
          "MEDGEN:725846",
          "MESH:C535293",
          "Orphanet:100057",
          "SCTID:403607004",
          "UMLS:C1304495"
        ],
        "synonyms": [
          "RAE",
          "Raas-blocker-induced angioedema",
          "Raas-blocker-induced angioneurotic edema",
          "Raas-blocker-induced angioneurotic oedema",
          "renin-angiotensin-aldosterone system-blocker-induced angioneurotic edema",
          "renin-angiotensin-aldosterone system-blocker-induced angioneurotic oedema",
          "AEACEI",
          "angioedema induced by ACE inhibitors, susceptibility to",
          "reactive angioendotheliomatosis",
          "susceptibility to angioedema induced by ace inhibitors"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Renin-angiotensin-aldosterone system (RAAS)-blocker induced angioedema (RAE) is a type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway."
      },
      "child_count": 0,
      "reference_id": "MONDO:0015057"
    },
    {
      "id": 22758,
      "label": "acquired angioedema with C1Inh deficiency",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        19414
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0022196",
          "MEDGEN:1846342",
          "Orphanet:528663",
          "UMLS:C5848086"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ]
      },
      "child_count": 0,
      "reference_id": "MONDO:0033948"
    },
    {
      "id": 22784,
      "label": "vibratory angioedema",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        19414
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0017901",
          "MEDGEN:99175",
          "Orphanet:493348",
          "UMLS:C0473546",
          "icd11.foundation:1471948086"
        ],
        "categories": [
          {
            "ref": "MONDO:0002051",
            "name": "integumentary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "Vibratory angioedema is a rare, inherited or sporadic, urticaria characterized by localized, typically long-lasting (hours to days), initially pruritic, painful, normocutaneous or erythematous, mucosal and/or cutaneous edema which is triggered by vibration. Laryngeal snoring-induced swelling may be life-threatening."
      },
      "child_count": 0,
      "reference_id": "MONDO:0034556"
    }
  ],
  "roots": [
    {
      "id": 11639,
      "label": "angioedema"
    }
  ]
}