{
  "id": 8111,
  "label": "adrenal cortex carcinoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0006639",
  "properties": {
    "xrefs": [
      "DOID:3948",
      "DOID:3959",
      "DOID:660",
      "EFO:1000796",
      "GARD:0000558",
      "HP:0006744",
      "ICDO:8370/3",
      "MEDGEN:104917",
      "MedDRA:10001388",
      "NANDO:2200073",
      "NCIT:C9325",
      "NORD:733",
      "ONCOTREE:ACC",
      "Orphanet:1501",
      "SCTID:255035007",
      "UMLS:C0206686",
      "icd11.foundation:114092945"
    ],
    "synonyms": [
      "adrenal cortex cancer",
      "adrenal cortical tumors",
      "adrenal cortical tumours",
      "adrenocortical cancer",
      "cancer of the adrenal cortex",
      "malignant adrenocortical tumor",
      "malignant adrenocortical tumour",
      "malignant neoplasm of adrenal cortex",
      "malignant tumor of adrenal cortex",
      "malignant tumour of adrenal cortex",
      "ACC",
      "Adenoid Cystic Carcinoma",
      "adenocarcinoma, adrenocortical, malignant",
      "adrenal cortex adenocarcinoma",
      "adrenal cortex carcinoma",
      "adrenal cortical adenocarcinoma",
      "adrenal cortical carcinoma",
      "adrenal cortical carcinoma (morphologic abnormality)",
      "adrenocortical carcinoma",
      "adrenocortical carcinoma (disease)",
      "carcinoma of adrenal cortex",
      "carcinoma of the adrenal cortex",
      "carcinoma, adrenocortical, malignant",
      "cortical cell carcinoma"
    ],
    "categories": [
      {
        "ref": "MONDO:0002118",
        "name": "urinary system disorder"
      },
      {
        "ref": "MONDO:0004995",
        "name": "cardiovascular disorder"
      },
      {
        "ref": "MONDO:0005151",
        "name": "endocrine system disorder"
      }
    ],
    "definition": "A rare, usually large (greater than 5cm), malignant epithelial tumor arising from the adrenal cortical cells. Symptoms are usually related to the excessive production of hormones, and include Cushing's syndrome and virilism in women. Common sites of metastasis include liver, lung, bone, and retroperitoneal lymph nodes. Advanced radiologic procedures have enabled the detection of small tumors, resulting in the improvement of the 5-year survival."
  },
  "isLeaf": false,
  "isRoot": false,
  "child_count": 1,
  "parents": [
    {
      "id": 4233,
      "label": "vascular cancer",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4237,
        20321
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:175",
          "MEDGEN:264315",
          "MESH:D009383",
          "NCIT:C8538",
          "Orphanet:673466",
          "UMLS:C1458139"
        ],
        "synonyms": [
          "Haemangiomatous tumor",
          "Haemangiomatous tumour",
          "blood vessel neoplasm",
          "blood vessel tumor",
          "blood vessel tumor (morphologic abnormality)",
          "blood vessel tumor disorder",
          "blood vessel tumors",
          "blood vessel tumors (morphologic abnormality)",
          "blood vessel tumour",
          "blood vessel tumour (morphologic abnormality)",
          "blood vessel tumour disorder",
          "blood vessel tumours",
          "blood vessel tumours (morphologic abnormality)",
          "neoplasm of great vessel",
          "vascular tumors",
          "vascular tumours",
          "cancer of vasculature",
          "malignant blood vessel neoplasm",
          "malignant blood vessel tumor",
          "malignant blood vessel tumour",
          "malignant neoplasm of vasculature",
          "malignant vascular tumor",
          "malignant vascular tumour",
          "malignant vasculature neoplasm",
          "pulmonary artery cancer",
          "vasculature cancer",
          "leiomyosarcoma of the renal vein",
          "malignant tumor of pulmonary artery",
          "malignant tumor of pulmonary vein",
          "malignant tumour of pulmonary artery",
          "malignant tumour of pulmonary vein",
          "malignant great vessel tumour",
          "renal vein leiomyosarcoma",
          "vascular tissue neoplasm"
        ],
        "categories": [
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          }
        ],
        "definition": "A malignant neoplasm arising from the blood vessels."
      },
      "child_count": 14,
      "reference_id": "MONDO:0002095"
    },
    {
      "id": 4840,
      "label": "adrenal carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        3710,
        4843
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:3950",
          "GARD:0023252",
          "MESH:D018268"
        ],
        "synonyms": [
          "adrenal gland carcinoma",
          "carcinoma of adrenal gland"
        ],
        "categories": [
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A carcinoma involving a adrenal gland."
      },
      "child_count": 4,
      "reference_id": "MONDO:0002814"
    },
    {
      "id": 6814,
      "label": "renal cell carcinoma",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        6712,
        6923
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "DOID:4450",
          "EFO:0000681",
          "GARD:0013215",
          "HP:0005584",
          "ICD9:189.0",
          "MEDGEN:766",
          "MESH:D002292",
          "MedDRA:10067946",
          "NANDO:2200045",
          "NORD:1657",
          "ONCOTREE:RCC",
          "Orphanet:217071",
          "SCTID:702391001",
          "UMLS:C0007134"
        ],
        "synonyms": [
          "RCC",
          "renal cell carcinoma",
          "renal cell carcinoma (disease)",
          "kidney adenocarcinoma",
          "renal cell adenocarcinoma"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          }
        ],
        "definition": "A carcinoma that arises from glandular epithelial cells of the kidney"
      },
      "child_count": 22,
      "reference_id": "MONDO:0005086"
    },
    {
      "id": 20494,
      "label": "malignant tumor of adrenal cortex",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        4843,
        22943
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0025311",
          "MEDGEN:83425",
          "NCIT:C9327",
          "SCTID:371964008",
          "UMLS:C0346402"
        ],
        "synonyms": [
          "adrenal cortex cancer",
          "cancer of adrenal cortex",
          "malignant adrenal cortex neoplasm",
          "malignant adrenal cortex tumor",
          "malignant adrenal cortex tumour",
          "malignant adrenocortical neoplasm",
          "malignant adrenocortical tumor",
          "malignant adrenocortical tumour",
          "malignant neoplasm of adrenal cortex",
          "malignant neoplasm of the adrenal cortex",
          "malignant tumor of the adrenal cortex",
          "malignant tumour of the adrenal cortex"
        ],
        "categories": [
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "A cancer that involves the adrenal cortex."
      },
      "child_count": 2,
      "reference_id": "MONDO:0021312"
    }
  ],
  "children": [
    {
      "id": 10007,
      "label": "adrenocortical carcinoma, hereditary",
      "isLeaf": true,
      "isRoot": false,
      "parents": [
        5006,
        8111
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0015132",
          "MEDGEN:348508",
          "MESH:C565972",
          "OMIM:202300",
          "UMLS:C1859972"
        ],
        "synonyms": [
          "adrenocortical carcinoma, hereditary",
          "hereditary adrenal cortex carcinoma",
          "ADCC",
          "adrenocortical carcinoma, paediatric",
          "adrenocortical carcinoma, pediatric"
        ],
        "categories": [
          {
            "ref": "MONDO:0002118",
            "name": "urinary system disorder"
          },
          {
            "ref": "MONDO:0004995",
            "name": "cardiovascular disorder"
          },
          {
            "ref": "MONDO:0005151",
            "name": "endocrine system disorder"
          }
        ],
        "definition": "An instance of adrenal cortex carcinoma that is caused by an inherited modification of the individual's genome."
      },
      "child_count": 0,
      "reference_id": "MONDO:0008734"
    }
  ],
  "roots": [
    {
      "id": 4233,
      "label": "vascular cancer"
    },
    {
      "id": 4840,
      "label": "adrenal carcinoma"
    },
    {
      "id": 6814,
      "label": "renal cell carcinoma"
    },
    {
      "id": 20494,
      "label": "malignant tumor of adrenal cortex"
    }
  ]
}