{
  "id": 17181,
  "label": "extraventricular neurocytoma",
  "model": {
    "label": "Mondo Disease Ontology (MONDO)",
    "source": 0
  },
  "type_id": 0,
  "reference_id": "MONDO:0016727",
  "properties": {
    "xrefs": [
      "DOID:0081314",
      "GARD:0020727",
      "ICDO:9506/1",
      "MEDGEN:457401",
      "NCIT:C92555",
      "ONCOTREE:EVN",
      "Orphanet:251927",
      "SCTID:716787002",
      "UMLS:C2985175"
    ],
    "synonyms": [
      "EVN",
      "extraventricular neurocytoma (WHO grade II)"
    ],
    "categories": [
      {
        "ref": "MONDO:0005071",
        "name": "nervous system disorder"
      }
    ],
    "definition": "Extraventricular neurocytoma (EVN), a variant of central neurocytoma, is a rare neuronal neoplasm, composed of round cells with neuronal differentiation, which is located outside of the ventricular system, usually within the spinal cord or cerebral hemispheres and that manifests with headache, nausea, vomiting, complex partial seizures or focal neurological deficits. In some cases it may exhibit atypical features consistent with aggressive clinical behavior."
  },
  "isLeaf": true,
  "isRoot": false,
  "child_count": 0,
  "parents": [
    {
      "id": 17182,
      "label": "mixed neuronal-glial tumor",
      "isLeaf": false,
      "isRoot": false,
      "parents": [
        20418
      ],
      "type_id": 0,
      "properties": {
        "xrefs": [
          "GARD:0020728",
          "MEDGEN:105377",
          "NCIT:C4747",
          "Orphanet:251934",
          "UMLS:C0474844",
          "icd11.foundation:1792897751"
        ],
        "synonyms": [
          "neuronal and Glio-neuronal neoplasm",
          "neuronal and Glio-neuronal tumor",
          "neuronal and Glio-neuronal tumour",
          "neuronal and mixed neuronal-glial tumor",
          "neuronal and mixed neuronal-glial tumors",
          "neuronal and mixed neuronal-glial tumour",
          "neuronal and mixed neuronal-glial tumours"
        ],
        "categories": [
          {
            "ref": "MONDO:0005071",
            "name": "nervous system disorder"
          }
        ],
        "definition": "A group of central nervous system neoplasms with a variable amount of neuronal and, less consistently, glial differentiation. They occur at a low frequency and usually carry a favorable prognosis. Representative examples include dysplastic cerebellar gangliocytoma, desmoplastic infantile ganglioglioma, desmoplastic infantile astrocytoma, and dysembryoplastic neuroepithelial tumor. (Adapted from WHO)"
      },
      "child_count": 12,
      "reference_id": "MONDO:0016729"
    }
  ],
  "children": [],
  "roots": [
    {
      "id": 17182,
      "label": "mixed neuronal-glial tumor"
    }
  ]
}